Brunity
DISEASE

Alkaptonuria

Overview

Nitisinone acts as an inhibitor of the enzyme 4-hydroxyphenyl pyruvic acid and therefore can reduce the formation of HGA. Based on this action, it can be expected that treatment of AKU patients with nitisinone may therefore reduce the consequences of the disorder, especially the joint destruction and the ochronosis of for instance the eye which develops with long-standing disease

Brunity
DISEASE

Tyrosinemia

Overview

Nitisinone is a hydroxyphenylpyruvate dioxygenase inhibitor used as an adjunct to dietary restrictions for the treatment of hereditary tyrosinemia type 1 (HT-1), which causes intolerance to tyrosine containing foods.

PKU A formula
DISEASE

Overview

Food for special medical purposes and must be used under medical supervision.

Comida-PKU A formula is an amino acid based powdered phenylalanine free formula containing other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals, trace elements, arachidonic acid (ARA) and docosahexaenoic acid (DHA).

PKU B (concentrate)
DISEASE

Overview

Food for special medical purposes and must be used under medical supervision.

Comida-PKU B is a phenylalanine free concentrated protein supplement, enriched with vitamins, minerals and trace elements.

PKU B formula
DISEASE

Overview

Food for special medical purposes and must be used under medical supervision.

Comida-PKU B formula is an amino acid based powdered phenylalanine free formula containing other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements.

PKU B/ A Formula/ B Formula
DISEASE

Overview

It is an amino acid based powdered phenylalanine free formula containing other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals, trace elements, arachidonic acid (ARA) and docosahexaenoic acid (DHA).

PKU Express 15/20
DISEASE

Overview

Express is a range of powdered protein substitutes, free from the offending amino acid(s). Express contains essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. It is also available for PKU, MSUD, HCU and TYR.

PKU express 15 Plus & 20 Plus
DISEASE

Overview

Food for special medical purposes and must be used under medical supervision.

PKU express plus is a powdered phenylalanine free* protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and docosahexaenoic acid (DHA). Flavoured options: with sugar and sweeteners.

PKU express plus 15 & 20
DISEASE

Overview

PKU express plus is a powdered phenylalanine free* protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and docosahexaenoic acid (DHA). Flavoured options: with sugar and sweeteners.

PKU express15 & 20
DISEASE

Overview

Food for special medical purposes and must be used under medical supervision.

PKU express plus is a powdered phenylalanine free* protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and docosahexaenoic acid (DHA). Flavoured options: with sugar and sweeteners.